Pulmonary Lymphangiomyomatosis Treated by Single Lung Transplantation

Authors:
  • HMHerve Mal
    Herve Mal
  • GJGilles Jebrak
    Gilles Jebrak
  • CDChristian Darne
    Christian Darne
  • EMEmmanuel Meeus
    Emmanuel Meeus
  • FDFrederic Dubois
    Frederic Dubois
  • MLMaurizio Luisetti
    Maurizio Luisetti
  • MFMichel Fournier
    Michel Fournier
  • RPRene Pariente
    Rene Pariente
  • BABernard Andreassian
    Bernard Andreassian

Abstract
Pulmonary lymphangiomyomatosis is a rare disease resistant to almost all medical treatments to date. We describe the case of a 44-yr-old woman with end-stage pulmonary lymphangiomyomatosis who was treated by single-lung transplantation. The patient is doing well in her sixteenth post-transplantation month and has a marked improvement in her pulmonary function tests and walking distance as compared with preoperative values, and she is enjoying an unrestricted life-style.

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