Survival of a child with spinal muscular atrophy and acute respiratory distress syndrome
Authors:
- 10 April 2015
- journal article
- research article
- Published by Wiley in Pediatric Pulmonology
- Vol. 50 (8) , E29-E31
Abstract
Summary: Spinal muscular atrophy (SMA), a lower motor neuron anterior horn cell disease, causes significant respiratory morbidity and mortality in children. Acute respiratory distress syndrome (ARDS) accounts for 1–4% of all Pediatric Intensive Care Unit (PICU) admissions. Management outcomes for ARDS in patients with SMA have not been described. We present the case of a 5‐year‐old boy with Type II SMA and ARDS requiring invasive mechanical ventilation. He improved with meticulous management of mechanical ventilation, airway clearance, fluid/nutrition, and sedation/analgesia. He was successfully extubated after 14 days of invasive mechanical ventilation and discharged home after a 20 day hospitalization. Pediatr Pulmonol. 2015; 50:E29–E31.Keywords
Funding Information
- none reported
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