Nummular keratopathy in a patient with Hyper-IgD Syndrome
Open Access
- 5 August 2009
- journal article
- Published by Springer Nature in Pediatric Rheumatology
- Vol. 7 (1) , 14
Abstract
To report a case of recurrent nummular keratitis in a pediatric patient with Hyperimmunoglobulinemia D syndrome. A retrospective chart review. A 14-year-old boy with Hyperimmunoglobulinemia D syndrome (HIDS) presented with photophobia and ocular irritation concomitant with disease exacerbation. He was found on exam to have significant nummular keratitis, which responded to a short course of topical steroids. Despite acute response to local immunosuppression, the patient had several recurrent attacks and eventually developed a large corneal scar and decreased vision. After initiation of infliximab therapy his ocular sequelae improved dramatically and his vision returned to 20/20. One possible form of end-organ damage associated with HIDS is vision threatening nummular keratopathy.Keywords
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