Clinical Presentation and Features of Juvenile-Onset Huntington’s Disease: A Systematic Review
- 30 April 2019
- journal article
- review article
- Published by SAGE Publications in Journal of Huntington's Disease
- Vol. 8 (2) , 171-179
Abstract
Background: Juvenile-onset Huntington’s disease (JHD) is defined by onset at the age of 20 or younger and represents approximately 5% of all HD cases. Patients with JHD present with a broad range of symptoms and signs that only overlap partially withKeywords
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