Cancer and Lhermitte-Duclos disease are common in Cowden syndrome patients
Open Access
- 17 June 2010
- journal article
- Published by Springer Nature in Hereditary Cancer in Clinical Practice
- Vol. 8 (1) , 6
Abstract
Cancer risk and Lhermitte-Duclos disease (LDD) risk estimates for Cowden syndrome (CS) are broad and based on a small number of patients. Risk estimates are vital to the development of diagnostic criteria, genetic counseling, and cancer surveillance. To further elaborate and estimate the risks associated with CS, a large cohort of patients was evaluated.Keywords
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