Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome
Open Access
- 1 March 2018
- journal article
- research article
- Published by Oxford University Press (OUP) in Oxford Medical Case Reports
- Vol. 2018 (3) , 96-99
Abstract
Hereditary haemorrhagic telangiectasia (HHT), also known as Osler–Weber–Rendu syndrome, is a rare autosomal dominant vascular disorder. Patients with HHT may present with a wide spectrum of clinical manifestations, some considered to be life-threatening. We present the case of a 53-year-old male who presented with massive haemoptysis. Chest computed tomography scan was remarkable for a large anterior, left lower lobe arteriovenous malformation. The patient underwent a pulmonary angiogram with embolization of a large left lung arteriovenous malformation, which proved to be successful in controlling the bleeding.Keywords
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