Cardiac manifestations in Emery–Dreifuss muscular dystrophy
Authors:
- 2 December 2018
- journal article
- editorial
- Published by CMA Impact Inc. in Canadian Medical Association Journal
- Vol. 190 (48) , E1414-E1417
Abstract
KEY POINTS A 35-year-old man with a known history of Emery–Dreifuss muscular dystrophy called emergency medical services (EMS) while at work one morning, reporting palpitations, lightheadedness, fatigue and a rapid heart rate. On arrival by EMS, his pulse was documented at 195–200 beats/min, andKeywords
This publication has 10 references indexed in Scilit:
- Management of Cardiac Involvement Associated With Neuromuscular Diseases: A Scientific Statement From the American Heart AssociationCirculation, 2017
- Arrhythmias in the Muscular DystrophiesCardiac Electrophysiology Clinics, 2015
- Prevalence of Muscular Dystrophies: A Systematic Literature ReviewNeuroepidemiology, 2014
- Implantable cardioverter-defibrillators in lamin A/C mutation carriers with cardiac conduction disordersHeart Rhythm, 2013
- Emery–Dreifuss muscular dystrophy2011
- Clinical outcomes after cardiac transplantation in muscular dystrophy patientsThe Journal of Heart and Lung Transplantation, 2010
- Management of Cardiac Involvement in NeuroMuscular Diseases: ReviewThe Open Cardiovascular Medicine Journal, 2008
- Echocardiographic assessment of left ventricular morphology and function in patients with Emery–Dreifuss muscular dystrophyInternational Journal of Cardiology, 2005
- Clinical Relevance of Atrial Fibrillation/Flutter, Stroke, Pacemaker Implant, and Heart Failure in Emery-Dreifuss Muscular DystrophyStroke, 2003
- Cardiac involvement in Becker's muscular dystrophy, necessitating heart transplantation, 6 years before apparent skeletal muscle involvementNeuromuscular Disorders, 1999