Cardiac involvement in Erdheim- Chester disease: MRI findings and literature revision
Open Access
- 1 September 2015
- journal article
- case report
- Published by SAGE Publications in Acta Radiologica Open
- Vol. 4 (9)
Abstract
Erdheim-Chester disease (ECD) is a rare form of non-Langerhans cell histiocytosis, characterized by the involvement of several organs. The lesions may be skeletal or extra-skeletal: in particular, long bones, skin, lungs, and the cardiovascular and the central nervous systems can be affected. In this report, we describe a case of a 34-year-old man, who came to our observation with symptomatic ECD, for a correct assessment of the degree of cardiac involvement through magnetic resonance imaging (MRI).Keywords
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