Hallervorden‐spatz syndrome: Clinical and magnetic resonance imaging correlations
Authors:
- 1 November 1988
- journal article
- research article
- Published by Wiley in Annals of Neurology
- Vol. 24 (5) , 692-694
Abstract
Two women with a presumptive diagnosis of Hallervor‐den‐Spatz syndrome had a combination of dystonia and parkinsonism. One had retinitis pigmentosa. Neuropsychological testing revealed Decemberreased verbal fluency and visuoconstructional and motor deficits. Magnetic resonance imaging performed with a high‐field‐strength unit (1.5 Tesla) showed striking abnormalities in the globus pallidus bilaterally (“eye‐of‐the‐tiger” sign). Magnetic resonance imaging may prove useful in the diagnosis of Hallervorden‐Spatz syndrome.Keywords
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