Update in Cystic Fibrosis 2013

This publication has 46 references indexed in Scilit:

• Air Trapping and Airflow Obstruction in Newborn Cystic Fibrosis Piglets
  American Journal of Respiratory and Critical Care Medicine, 2013
• Efficacy and Safety of Ivacaftor in Patients Aged 6 to 11 Years with Cystic Fibrosis with a G551D Mutation
  American Journal of Respiratory and Critical Care Medicine, 2013
• Personalized Medicine in Cystic Fibrosis: Dawning of a New Era
  American Journal of Respiratory and Critical Care Medicine, 2012
• Reduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung
  Nature, 2012
• A CFTR Potentiator in Patients with Cystic Fibrosis and theG551DMutation
  New England Journal of Medicine, 2011
• A new role for bicarbonate in mucus formation
  American Journal of Physiology-Lung Cellular and Molecular Physiology, 2010
• Cystic Fibrosis Pigs Develop Lung Disease and Exhibit Defective Bacterial Eradication at Birth
  Science Translational Medicine, 2010
• Submucosal gland secretions in airways from cystic fibrosis patients have normal [Na⁺] and pH but elevated viscosity
  Proceedings of the National Academy of Sciences, 2001
• Activation of NF-kappaB by adherent Pseudomonas aeruginosa in normal and cystic fibrosis respiratory epithelial cells.
  Journal of Clinical Investigation, 1998
• Neutrophil elastase in respiratory epithelial lining fluid of individuals with cystic fibrosis induces interleukin-8 gene expression in a human bronchial epithelial cell line.
  Journal of Clinical Investigation, 1992