Sanjad-Sakati Syndrome Dental Management: A Case Report
Open Access
- 21 February 2013
- journal article
- case report
- Published by Wiley in Case Reports in Dentistry
- Vol. 2013, 1-4
Abstract
Sanjad-Sakati syndrome (SSS) is a rare genetic disorder with autosomal recessive pattern of inheritance characterized by hypoparathyroidism, sever growth failure, mental retardation, susceptibility to chest infection, and dentofacial anomalies. A child with SSS was referred to the dental departmentseeking dental help for sever dental caries which was attributed to his dietary habits and quality of dental tissues. Full restorative rehabilitation was done under general anesthesia. Two years later, the child presented with recurrent caries affecting uncrowned teeth. High carries recurrence rate was blamed for the nutritional habits endorsed by the parents. Only steel crowned teeth survived such hostile oral environment which suggested shifting of treatment strategy towards full coverage restorations instead of classical cavity preparations and fillings during a second attempt for dental treatment under general anesthesia and for the dental treatment of two cousins of the same child. The author recommends effective health education for parents including the nature of their child’s genetic disorder, nutritional needs, and dental health education to improve the life style of such children.Keywords
This publication has 9 references indexed in Scilit:
- Sanjad-Sakati Syndrome in Omani children.2010
- Case report: Sanjad--Sakati syndrome: dental findings and treatment.2010
- Consanguinity and reproductive health among ArabsReproductive Health, 2009
- Anesthesia management for the child with Sanjad–Sakati syndromePediatric Anesthesia, 2006
- The dentofacial features of Sanjad–Sakati syndrome: a case reportInternational Journal of Paediatric Dentistry, 2004
- Hypoparathyroidism, retarded growth and development, and dysmorphism or Sanjad-Sakati syndrome: an Arab disease reminiscent of Kenny-Caffey syndromeJournal of Medical Genetics, 2000
- The syndrome of hypoparathyroidism, severe growth failure, developmental delay and distinctive faciesClinical Dysmorphology, 1997
- A new syndrome of congenital hypoparathyroidism, severe growth failure, and dysmorphic features.Archives of Disease in Childhood, 1991
- Short stature, mental retardation, and hypoparathyroidism: a new syndrome.Archives of Disease in Childhood, 1990